Arq. Bras. Cardiol. 2020; 115(1 suppl 1): 37-39
Case 6/2020 – 16-Year-Old Adolescent with Severe Pulmonary Stenosis At Valvar Level, After Correction of Truncus Arteriosus using the Barbero-Marcial Technique in the First Month of Life
Edmar Atik
, Miguel Barbero-Marcial
Clinical Data
The newborn, in heart failure with truncus arteriosus type I, underwent repair at 15 days of age, weighing 2800 g. of body weight, by the Barbero-Marcial technique. At that time, the right ventricular outflow tract was approached directly with the pulmonary trunk and a monocusp valve was placed in the pulmonary position.
The evolution was adequate, with heart failure control, and he remained asymptomatic and showed normal physical development. The clinical examination ruled out residual lesions, such as pulmonary valve insufficiency. Over time, while asymptomatic, a systolic murmur was identified in the pulmonary area, of progressive intensity, together with an increasing pressure gradient in the region of the pulmonary monocusp. At 2 years of age, it was 25 mmHg; at 5 years, 34 mm Hg; at 7 years, it was 40; at 13 years it was 90 and at 16 years it was 149 mmHg. The patient did not use any specific medications.
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