Arq. Bras. Cardiol. 2024; 121(5): e20230576
Idiopathic Constrictive Pericarditis with Restrictive “Vertical Double Ring” Structure in a Patient with Right Ventricular Outflow Tract Stenosis
Introduction
Constrictive pericarditis is defined as an inflammatory process of the fibrous and serous layers of the pericardium that leads to pericardial thickening and compression of the cardiac chambers, ultimately resulting in a significant reduction in cardiac function. Tuberculous pericarditis remains the leading cause of constrictive pericarditis worldwide, especially in the remote rural areas of eastern countries where the level of health care and services is relatively backward. Other causes include postcardiotomy, connective tissue diseases, postmediastinal irradiation, uremia, and idiopathic. Herein, we present a rare case of idiopathic constrictive pericarditis with severe right ventricular outflow tract (RVOT) stenosis. The thickened tissue formed a restrictive “vertical double ring” structure, involving the atrioventricular sulcus and ventricles that led to compression of the cardiac chambers.
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