Significant advances in understanding cardiac amyloidosis (CA) have been made in recent years, leading to a thorough reformulation of its clinical significance. In addition to convincing evidence that CA is a relatively common cause of heart failure with preserved ejection fraction (HFpEF), we are witnessing the emergence of specific therapies that can change the course of the disease and prolong the survival of affected patients.
In parallel, relevant advances in cardiovascular imaging techniques have greatly contributed to earlier and more accurate identification of the disease. Cardiac scintigraphy with bone-seeking radiotracers has allowed non-invasive diagnosis of transthyretin (TTR) cardiac amyloidosis (ATTR-CA), eliminating the need for endomyocardial biopsy, which has greatly simplified the diagnostic flow.
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Position Statement on Diagnosis and Treatment of Cardiac Amyloidosis – 2021
SimõesMV, FernandesF, Marcondes-BragaFG, ScheinbergP, CorreiaEB, RohdeLEP, BacalF, et al. Position Statement on Diagnosis and Treatment of Cardiac Amyloidosis – 2021. Arq. Bras. Cardiol. 2021;117(3):561-98.
Simões,Marcus V. and Fernandes,Fabio and Marcondes-Braga,Fabiana G. and Scheinberg,Philip and Correia,Edileide de Barros and Rohde,Luis Eduardo P. and Bacal,Fernando and Alves,Silvia Marinho Martins and Mangini,Sandrigo and Biolo,Andréia and Beck-da-Silva,Luis and Szor,Roberta Shcolnik and Marques Junior,Wilson and Oliveira,Acary Souza Bulle and Cruz,Márcia Waddington and Bueno,Bruno Vaz Kerges and Hajjar,Ludhmila Abrahão and Issa,Aurora Felice Castro and Ramires,Felix José Alvarez and Coelho Filho,Otavio Rizzi and Schmidt,André and Pinto,Ibraim Masciarelli Francisco and Rochitte,Carlos Eduardo and Valicelli,Flávio Henrique and Vieira,Marcelo Luiz Campos and Mesquita,Cláudio Tinoco and Ramos,Celso Dario and Soares-Junior,José and Romano,Minna Moreira Dias and Mathias Junior,Wilson and Garcia Junior,Marcelo Iório and Montera,Marcelo Westerlund and Melo,Marcelo Dantas Tavares de and Silva,Sandra Marques e and Garibaldi,Pedro Manoel Marques and Alencar Neto,Aristóteles Comte de and Lopes,Renato Delascio and Ávila,Diane Xavier de and Viana,Denizar and Saraiva,José Francisco Kerr and Canesin,Manoel Fernandes and Oliveira,Glaucia Maria Moraes de and Mesquita,Evandro Tinoco. Position Statement on Diagnosis and Treatment of Cardiac Amyloidosis – 2021. Arq. Bras. Cardiol. [online]. 2021, vol. 117, n. 3, [cited 2025-10-25], pp.561-598. Available from: <https://abccardiol.org/en/article/position-statement-on-diagnosis-and-treatment-of-cardiac-amyloidosis-2021/>. ISSN 0066-782X.